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<article xlink="http://www.w3.org/1999/xlink" dtd-version="1.0" article-type="allergy-and-immunology" lang="en">
<front>
<journal-meta>
<journal-id journal-id-type="publisher">JOHS</journal-id>
<journal-id journal-id-type="nlm-ta">Journ of Health Scien</journal-id>
<journal-title-group>
<journal-title>Journal of HealthCare Sciences</journal-title>
<abbrev-journal-title abbrev-type="pubmed">Journ of Health Scien</abbrev-journal-title>
</journal-title-group>
<issn pub-type="ppub">2231-2196</issn>
<issn pub-type="opub">0975-5241</issn>
<publisher>
<publisher-name>Radiance Research Academy</publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id pub-id-type="publisher-id">439</article-id>
<article-id pub-id-type="doi">http://dx.doi.org/10.52533/JOHS.2025.51003</article-id>
<article-id pub-id-type="doi-url"/>
<article-categories>
<subj-group subj-group-type="heading">
<subject>Allergy and Immunology</subject>
</subj-group>
</article-categories>
<title-group>
<article-title>Challenges and Solutions in Full-Mouth Rehabilitation of a Pediatric Hypohidrotic Ectodermal Dysplasia Patient. A Case Report
</article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname>Alsharif</surname>
<given-names>Ahmed N.</given-names>
</name>
</contrib>
<contrib contrib-type="author">
<name>
<surname>Basudan</surname>
<given-names>Osamah A.</given-names>
</name>
</contrib>
<contrib contrib-type="author">
<name>
<surname>Alhajrassi</surname>
<given-names>Sahar K.</given-names>
</name>
</contrib>
<contrib contrib-type="author">
<name>
<surname>Albadawi</surname>
<given-names>Emad A.</given-names>
</name>
</contrib>
</contrib-group>
<pub-date pub-type="ppub">
<day>22</day>
<month>10</month>
<year>2025</year>
</pub-date>
<volume>5</volume>
<issue>10</issue>
<fpage>513</fpage>
<lpage>520</lpage>
<permissions>
<copyright-statement>This article is copyright of Popeye Publishing, 2009</copyright-statement>
<copyright-year>2009</copyright-year>
<license license-type="open-access" href="http://creativecommons.org/licenses/by/4.0/">
<license-p>This is an open-access article distributed under the terms of the Creative Commons Attribution (CC BY 4.0) Licence. You may share and adapt the material, but must give appropriate credit to the source, provide a link to the licence, and indicate if changes were made.</license-p>
</license>
</permissions>
<abstract>
<p>Background: Ectodermal dysplasia syndromes (EDs) are rare genetic disorders that affect ectodermal-derived tissues, including teeth, hair, and sweat glands. Hypohidrotic ectodermal dysplasia (HED) is the most common type, typically characterized by a reduced ability to sweat (hypohidrosis), along with significant dental anomalies. Dental abnormalities such as hypodontia or anodontia, misshapen teeth, and underdeveloped jaws are among the most prominent features, often resulting in functional, esthetic, and psychological concerns. Early dental diagnosis and prosthetic management are essential for enhancing oral function, facial appearance, and overall quality of life. This case report highlights the dental challenges and rehabilitation of a pediatric patient with ED.
Case Presentation: An 8-year-old boy, diagnosed with hypohidrotic ectodermal dysplasia at age 4, presented with dry skin, heat intolerance, sparse hair, and multiple missing teeth with conical-shaped dentition. He had no allergies and showed normal growth patterns. Clinical examination revealed typical features of ED, including oligodontia, microdontia, taurodontism, generalized gingivitis, and reduced salivary flow. Treatment included behavioral guidance, preventive care (fluoride application and dietary advice), and restorative work under local anesthesia. Ongoing care involves regular follow-ups, radiographs, and prosthetic adjustments. The patient showed improved oral function, aesthetics, and psychosocial well-being, with no complications noted during follow-up.
Conclusion: Dental management of ectodermal dysplasia requires early, multidisciplinary care to restore function, aesthetics, and quality of life. Early diagnosis and prosthetic rehabilitation improve outcomes. Treatment should align with growth and individual needs. Overdentures and conservative restorations aid development, while implants are delayed. Consistent follow-ups and excellent oral hygiene are vital for long-term treatment success.
</p>
</abstract>
<kwd-group>
<kwd>Ectodermal Dysplasia</kwd>
<kwd> Hypohidrotic Ectodermal Dysplasia</kwd>
<kwd> Oligodontia</kwd>
<kwd> Overdenture</kwd>
<kwd> Craniofacial Abnormalities</kwd>
</kwd-group>
</article-meta>
</front>
</article>